Primary rhabdomyosarcoma (RMS) of breast and RMS, metastatic to breast are rare entities with limited case reports in literature. Here, we report a case of primary rhabdomyosarcoma of breast in an adolescent girl which was metastatic at presentation. She presented with progressively increasing lump in right breast with difficulty in breathing. Histopathology was suggestive of solid variant of alveolar type/embryonal carcinoma (undifferentiated type). Immunohistochemical reports were positive for muscle markers Vimentin and Myf-4, making definitive diagnosis of RMS. Patient had fast progression of disease and died after first cycle of chemotherapy.